A Case report of the largest Right Ventricular Hémangioma
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Background:
Primary cardiac tumors are rare and often asymptomatic or present with unspecific symptoms.
Benign cardiac tumors of vascular origin are especially rare, with only few existing data in the literature.
Case presentation:
A 26-year-old woman presented cardiac symptoms like palpitations four month earlier; he started complaining of fatigue and mild exercise dyspnea. His cardiologist discovered a systolic murmur. Echocardiography showed a large right ventricular mass, which engaged in the tricuspid valve in hoes generating a transtricuspidien gradient of 15 mmHg,
Our patient then underwent cardiovascular magnetic resonance (CMR) imaging and a thoracoabdominopelvic CT scan the day after admission, which revealed that there isn’t enormous than this mass
The surgeons were preparing to operate the patient but the patient's biological assessment was disrupted, and
2 days later a cardiogenic shock state requiring administration of dobutamine without improvement.
The evolution was marked by the installation of a severe bradycardia with impaired consciousness with a GCS 3 having motivated the family to take agonizing to his parental home, the patient unfortunately died on his arrival home.
Conclusion:
We conclude that MRI is advantageous over a combination of TTE and TEE for the detection and complete morphological and functional evaluation (hemodynamic effects) of cardiac masses.
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